Sigmoid Vaginoplasty in Type 2 Mayer–Rokitansky–Kuster–Hauser Syndrome: A Rare Classical Case

Abstract

Among the abnormalities in paramesonephric duct structure in Mayer–Rokitansky–Kuster; the most common abnormality is vaginal aplasia. Here, a case report of a 19-year-old girl, with MRKHS-2 having vaginal agenesis, is presented. The uterus was atrophic, and the ovaries were normal. There was also an ectopic solitary kidney lying in the pelvis on the left side, unilateral polydactyly, aortic regurgitation, and fused L2, L3, and L4 vertebrae. Sigmoid vaginoplasty was done. The postoperative period was uneventful.